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Cardiac muscle Myotonic Dystrophy Myotonic Dystrophy type 1 Dystrophie Myotonique Thérapie génique Glutamate Antisense oligonucleotides Astrocyte Skeletal muscle CTG repeat instability Myotonic dystrophy Acetylcholinesterase knockout mouse Motoneuron Trinucleotide repeat expansion AAV Hypoxia Humans CRISPR/Cas9 Muscular dystrophy Alternative splicing Heart Central nervous system Mice Myelin Duchenne muscular dystrophy CMS Acute coronary syndrome Aging Glucocorticoids Muscle GABA Desmin Transcriptomics Diaphragm Myotonic dystrophy mouse models Gene therapy Glial cells Centronuclear myopathy PacBio Mouse models Antisense oligonucleotide Quantitative microdialysis Lc3 Dystrophin Animals Brain dysfunction GSK3␤ Oligodendrocytes Myostatin In vivo CTG repeat contractions Cell culture model Therapy KNOCKOUT MICE Fibrosis DM1 DMSXL mice Dilated cardiomyopathy Neuron Myotonic Dystrophy Type 1 Astrocytes CTG repeats DMPK Brain Long read sequencing Exercice CONGENITAL MYATHENIC SYNDROME Male Exercise CRISPRi Genotype phenotype correlation Trinucleotide Repeat Expansion Maximal force Glucocorticoid-receptor RNA splicing BIOLOGIE MOLECULAIRE Intermediate filament ACETYLCHOLINESTERASE Gene Therapy Oligodendrocyte Mouse model Myotonic dystrophy type 1 Cytoskeleton MBNL Cell penetrating peptide RNA interference Transgenic mouse model Cell model Transgenic mouse Gene editing Dynamin 2 Dystrophie myotonique Expression PCR Autophagy Heart failure Knockout RNA biology ARN Acetylcholinesterase deficiency